Abstract: First case of Ewing's sarcoma of kidney was reported in the year 1975. They are rarely found high-grade malignant potentials, with poor prognosis. Ewing sarcoma/PNET of the kidney is sparse, with less than 100 cases reported in the literature. We are hereby presenting a case of 19 years old female with complaints of vague abdominal pain.CECT abdomen and pelvis revealed a 16x16x15cms heterogenous hypoechoic mass arising from upper pole of left kidney.Radical nephrectomy was done. .Immuno-histochemistry shows positivity for CD99, FLI-1 and negative for WT-1.Morphology in correlation with IHC is consistent with Ewing's sarcoma family of tumours.6 cycles of chemotherapy with VAC regimen was planned and patient was kept on regular follow-up..
Key words: CD99, Ewings sarcoma family of tumors, Immuno-histochemistry, Radical nephrectomy, VAC regimen
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